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Open Access
CC BY 4.0 · Rev Bras Ginecol Obstet 2018; 40(11): 722-725
DOI: 10.1055/s-0038-1673677
Case Report
Thieme Revinter Publicações Ltda Rio de Janeiro, Brazil

Fetal Noncompaction Cardiomyopathy and Histologic Diagnosis of Spongy Myocardium: Case Report and Review of the Literature

Authors

  • Luigi Nappi

    1   Department of Medical and Surgical Sciences, Institute of Obstetrics and Gynecology, Università di Foggia, Foggia, Italy

  • Lorenzo Vasciaveo

    1   Department of Medical and Surgical Sciences, Institute of Obstetrics and Gynecology, Università di Foggia, Foggia, Italy

  • Felice Sorrentino

    1   Department of Medical and Surgical Sciences, Institute of Obstetrics and Gynecology, Università di Foggia, Foggia, Italy

  • Gennaro Scutiero

    2   Section of Obstetrics and Gynecology, Department of Morphology, Surgery and Experimental Medicine, Università degli Studi di Ferrara, Ferrara, Italy

  • Piergiorgio Iannone

    2   Section of Obstetrics and Gynecology, Department of Morphology, Surgery and Experimental Medicine, Università degli Studi di Ferrara, Ferrara, Italy

  • Pantaleo Greco

    2   Section of Obstetrics and Gynecology, Department of Morphology, Surgery and Experimental Medicine, Università degli Studi di Ferrara, Ferrara, Italy
Further Information

Publication History

21 June 2018

09 August 2018

Publication Date:
11 October 2018 (online)

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Abstract

Noncompaction cardiomyopathy (NCCM) and left ventricular noncompaction (LVNC), in their isolated form, are rare cardiomyopathies. They are characterized by a thickened myocardium due to the presence of deep trabeculae recesses, and to thick trabeculae. This condition is associated with a variable clinical phenotype including heart failure, thromboembolism, and sudden death. We report a case of LVNC at 26 weeks and 4 days of gestation revised on the basis of what is currently reported in the literature. A review of the literature was performed to better describe this rare condition. Left ventricular noncompaction is a rare fetal condition and it should be suspected in case of cardiomyopathy.

Keywords

noncompaction cardiomyopathy - spongy myocardium - left ventricular noncompaction cardiomyopathy
 

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