Presentation of Intrahepatic Cholangiocarcinoma with Fulminant Hepatic Failure: A Case Report

Abstract

Fulminant hepatic failure as initial presentation due to diffuse parenchymal infiltration by cholangiocarcinoma is a rare entity. We present the case of a 49-year-old female patient who had a fatal outcome with acute liver failure due to diffuse intrahepatic cholangiocarcinoma. No definite mass lesion was identified on cross-sectional imaging. The final diagnosis was made on transjugular liver biopsy. This discussion highlights the possibility of infiltrative cholangiocarcinoma as a rare cause of fulminant hepatic failure.

Keywords

fulminant hepatic failure - intrahepatic cholangiocarcinoma - transjugular liver biopsy

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