Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances
in the ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or
hypotrichosis and palmoplantar hyperkeratosis is usually accompanied by a lack of
sweat glands and a partial or complete absence of primary and/or permanent dentition.
Two case reports illustrating the prosthetic rehabilitation of 2 young boys with anhidrotic
ectodermal dysplasia associated with severe anodontia are presented. Since the oral
rehabilitation of these cases is often difficult; particularly in pediatric patients,
treatment should be administered by a multidisciplinary team involving pediatric dentistry,
orthodontics, prosthodontics and oral-maxillofacial surgery. (Eur J Dent 2010;4:215-222)
Keywords
Anodontia - Prosthetic rehabilitation - Multidisciplinary management
