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CC BY 4.0 · European J Pediatr Surg Rep. 2019; 07(01): e79-e82
DOI: 10.1055/s-0039-1697925
Case Report
Georg Thieme Verlag KG Stuttgart · New York

An Unusual Case of Syringohydromyelia Presenting with Neurogenic Bladder

Antonella Geljic
1   Department of Paediatrics, Klinika za djecje bolesti Zagreb, Zagreb, Croatia
,
Slaven Abdovic
2   Department of Pediatric Nephrology, Klinika za djecje bolesti Zagreb Klinika za pedijatriju, Zagreb, Croatia
,
Fran Stampalija
3   Department of Pediatric Urology, Klinika za djecje bolesti Zagreb, Zagreb, Croatia
,
Lana Loncar
4   Department of Pediatric Neurology, Klinika za djecje bolesti Zagreb Klinika za pedijatriju, Zagreb, Croatia
,
Batos A. Tripalo
5   Department of Pediatric Radiology, Klinika za djecje bolesti Zagreb, Zagreb, Croatia
,
Martin Cuk
2   Department of Pediatric Nephrology, Klinika za djecje bolesti Zagreb Klinika za pedijatriju, Zagreb, Croatia
› Author Affiliations
Further Information

Publication History

02 January 2019

19 August 2019

Publication Date:
22 November 2019 (online)

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Abstract

We report the case of a 4-year-old boy who first presented with acute pyelonephritis at the age of 6 months. Diagnostic workup revealed high-grade bilateral vesicourethral reflux (VUR). At the age of 18 months, a bulking agent was used to treat bilateral VUR. Since the VUR persisted, an open bilateral Lich-Gregoir procedure was done at the age of 3 years. Immediately after surgery, he developed acute urinary retention with hydronephrosis that resolved with the placement of dwelling urinary catheter. After removal of the catheter urinary retention relapsed so placement of suprapubic urinary catheter was indicated since he did not have sensory loss. He was started with tamsulosin (α − 1-blocker) and prophylactic antibiotics. Urodynamics were performed and suggested bladder outlet obstruction. On the basis of previous urethroscopy and the absence of neurological sequelae, the differential diagnosis of Hinman syndrome was made. After removal of the suprapubic catheter, clean intermittent catheterization was started and α-blocker continued. However, magnetic resonance imaging of the brain and the spinal cord revealed syringohydromyelia extending from thoracic spine (Th5) to conus medullaris with 6 to 7 mm in diameter. Electromyoneurogram was normal. After a follow-up of 3 years, the hydronephrosis has resolved. The patient is on clean intermittent catherization and has no urinary tract infections.

Keywords

neurogenic bladder - syringohydromyelia - vesicourethral reflux
 

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