Abstract
Osteogenesis imperfecta (OI) is a genetic disorder of collagen resulting in a “fragile”
skeleton with increased fracture risk and other complications, dependent on the specific
variant. Pectus deformities of the chest wall, while not common, can be associated
with OI. The use of a pectus carinatum brace in a patient with OI poses unknown risks
for fractures and adverse treatment outcomes. We successfully applied external compression
bracing using the dynamic compression system to one such patient. This case illustrates
the ability to treat an OI patient with pectus carinatum using a nonsurgical brace,
without complications, resulting in an excellent cosmetic result.
Keywords
pectus carinatum - osteogenesis imperfecta - dynamic compression system
