Posterior Cloacal Variant with Clitorolabial Transposition and a Rectoperineal Fistula

Abstract

We present a case and discuss the management of a posterior cloacal variant not as yet described in the literature. A 5-week-old infant presented to our institution with a posterior cloacal variant and transposition of the clitoris and labia. After initial radiological investigations, staged operative intervention was performed over a 1-year period. This included an initial laparotomy (with drainage of hydrocolpos and formation of a colostomy), a left ureteric reimplantation and a posterior sagittal anorectoplasty due to a rectoperineal fistula. The child is under continued long-term follow-up by our specialist pediatric surgical team.

Keywords

posterior cloacal variant - anorectal malformation - cloaca

Publikationsverlauf

Eingereicht: 12. November 2020

Angenommen: 06. März 2021

Artikel online veröffentlicht:
18. Mai 2021

• References

• 1 Leditschke JF, Pena A. An unusual cloacal anomaly -late recognition and operative correction. Pediatr Surg Int 1991; 6: 52-55 . Available at: http://doi.org/10.1007/BF00174887
• 2 Peña A, Kessler O. Posterior cloaca: a unique defect. J Pediatr Surg 1998; 33 (03) 407-412
• 3 Peña A, Bischoff A, Breech L, Louden E, Levitt MA. Posterior cloaca--further experience and guidelines for the treatment of an unusual anorectal malformation. J Pediatr Surg 2010; 45 (06) 1234-1240
• 4 Komasara L, Bryks-Laszkowska A, Sroka M, Gołębiewski A, Czauderna P. A unique defect - persistent posterior cloaca: an example of staged genito-urinary and digestive tract reconstruction with an alternative vaginal creation using the urinary bladder wall. Int J Urol 2017; 24 (06) 468-471
• 5 Ahmed I, Kureel SN, Chandra N. Reverse (posterior) cloaca with congenital rectal stenosis and pseudohermaphrodism: a rare entity with rare association. BMJ Case Rep 2010; 2010: bcr0620103071