Primary Chylopericardium with Pulmonary Lymphedema

Introduction

About 100 cases of primary chylopericardium have been reported since Gloves and Effler first reported this disorder [[1]]. It is an extremely rare entity that accounts for only 3 % of all primary chylous disorders [[2]]. Many patients have symptoms of dyspnea or cough, but few have pulmonary lesions. We report a case of primary chylopericardium with pulmonary lesions that presented with interstitial opacities.

References

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