Rehabilitation in patients with cerebellar ataxias

Hsin Fen Chien; Marise Bueno Zonta; Janini Chen; Giovana Diaferia; Celiana Figueiredo Viana; Hélio Afonso Ghizoni Teive; José Luiz Pedroso; Orlando Graziani Povoas Barsottini

doi:10.1590/0004-282X-ANP-2021-0065

Arquivos de Neuro-Psiquiatria, Inhaltsverzeichnis

CC BY-NC-ND 4.0 · Arq Neuropsiquiatr 2022; 80(03): 306-315
DOI: 10.1590/0004-282X-ANP-2021-0065

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Rehabilitation in patients with cerebellar ataxias

Reabilitação em pacientes com ataxias cerebelares

Hsin Fen Chien

¹Universidade de São Paulo, Faculdade de Medicina, Departamento de Ortopedia e Traumatologia, São Paulo SP, Brazil.

,

Marise Bueno Zonta

²Universidade Federal do Paraná, Hospital de Clínicas, Departamento de Medicina Interna, Serviço de Neurologia, Unidade de Distúrbios do Movimento, Curitiba PR, Brazil.

,

Janini Chen

¹Universidade de São Paulo, Faculdade de Medicina, Departamento de Ortopedia e Traumatologia, São Paulo SP, Brazil.

,

Giovana Diaferia

³Universidade Federal de São Paulo, Departamento de Neurologia, Divisão de Neurologia Geral e Unidade de Ataxia, São Paulo SP, Brazil.

,

Celiana Figueiredo Viana

³Universidade Federal de São Paulo, Departamento de Neurologia, Divisão de Neurologia Geral e Unidade de Ataxia, São Paulo SP, Brazil.

,

Hélio Afonso Ghizoni Teive

²Universidade Federal do Paraná, Hospital de Clínicas, Departamento de Medicina Interna, Serviço de Neurologia, Unidade de Distúrbios do Movimento, Curitiba PR, Brazil.

,

José Luiz Pedroso

³Universidade Federal de São Paulo, Departamento de Neurologia, Divisão de Neurologia Geral e Unidade de Ataxia, São Paulo SP, Brazil.

,

Orlando Graziani Povoas Barsottini

³Universidade Federal de São Paulo, Departamento de Neurologia, Divisão de Neurologia Geral e Unidade de Ataxia, São Paulo SP, Brazil.

› Institutsangaben

Abstract

ABSTRACT

Cerebellar ataxias comprise a heterogeneous group of diseases characterized by motor and non-motor symptoms, which can be acquired, degenerative, or have a genetic cause, such as spinocerebellar ataxias (SCA). Usually, the genetic and neurodegenerative forms of cerebellar ataxias present a progressive and inevitable worsening of the clinical picture so that rehabilitation treatment is fundamental. Rehabilitation treatment includes physical therapy, respiratory therapy, speech, voice and swallowing therapy, occupational therapy, and new technologies, such as the use of exergames. The current treatment of patients with cerebellar ataxias, especially neurodegenerative forms, genetic or not, should include these different forms of rehabilitation, with the main objective of improving the quality of life of patients.

RESUMO

As ataxias cerebelares compreendem um grupo heterogêneo de doenças caracterizadas por sintomas motores e não motores, que podem ser adquiridas, degenerativas ou ter uma causa genética, como as ataxias espinocerebelares (AEC). Normalmente, as formas genéticas e neurodegenerativas de ataxias cerebelares apresentam uma piora progressiva e inexorável do quadro clínico e o tratamento com reabilitação é fundamental. O tratamento com reabilitação inclui a fisioterapia, fisioterapia respiratória, fonoterapia, terapia ocupacional e novas tecnologias, como o uso de exergames. O tratamento atual de pacientes com ataxias cerebelares, em particular as formas neurodegenerativas, genéticas ou não, deve incluir essas diferentes formas de reabilitação, com o objetivo principal de melhorar a qualidade de vida dos pacientes.

Keywords:

Cerebellar Ataxia - Rehabilitation - Physical Therapy Specialty - Speech Therapy - Occupational Therapy

Palavras-chave:

Ataxia Cerebelar - Reabilitação - Especialidade de Fisioterapia - Fonoterapia - Terapia Ocupacional

Volltext

Referenzen

References
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