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CC BY 4.0 · Revista Brasileira de Cirurgia Plástica (RBCP) – Brazilian Journal of Plastic Surgery 2024; 39(02): 217712352024rbcp0870pt
DOI: 10.5935/2177-1235.2024RBCP0870-PT
Relato de Caso

Serial lipectomy and liposuction for management of Madelung syndrome: About a case

Artikel in mehreren Sprachen: português | English
PEDRO HENRIQUE DE ARAÚJO SILVA 
1   Hospital das Clínicas da Universidade Federal de Pernambuco, Recife, PE, Brasil.
,
JAIRO ZACCHÊ DE SÁ 
1   Hospital das Clínicas da Universidade Federal de Pernambuco, Recife, PE, Brasil.
,
FLÁVIO JOSÉ TEIXEIRA ROCHA ATAÍDE DA MOTTA 
1   Hospital das Clínicas da Universidade Federal de Pernambuco, Recife, PE, Brasil.
,
HELENA GABRIELE ALVES CASTRO 
1   Hospital das Clínicas da Universidade Federal de Pernambuco, Recife, PE, Brasil.
,
VINICYUS EDUARDO MELO AMORIM 
2   Faculdade Pernambucana de Saúde, Recife, PE, Brasil.
,
ANDRESA DOS SANTOS VIANA 
3   Universidade Federal de Pernambuco, Recife, PE, Brasil.
,
LARISSA CARARETO BRAVIN 
3   Universidade Federal de Pernambuco, Recife, PE, Brasil.
,
PEDRO HENRIQUE PONTUAL 
2   Faculdade Pernambucana de Saúde, Recife, PE, Brasil.
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▪ ABSTRACT

Madelung’s disease is characterized by the symmetric and diffuse accumulation of adipose tissue with slow and progressive tumor growth. In this case report, a patient with this syndrome was treated at Hospital das Clínicas, in Recife, PE, to reduce the lipomatous content through a lipectomy. The patient presented large masses of elastic adipose tissue around the neck and supraclavicular region and the therapeutic proposal consisted of a two-stage surgery, with liposuction and anterior cervical lipectomy, followed by liposuction and posterior cervical lipectomy. Before surgery, a cardiological opinion was requested, which indicated an intermediate risk but did not contraindicate the procedure. Four days after surgery, the patient presented bruises and peripheral edema in the cervical surgical wound but was asymptomatic. Lipectomy and liposuction techniques are considered the most effective treatment methods for Madelung disease. However, the choice of surgery should be based on a comprehensive assessment of the severity of the disease, location of the mass, and patient expectations, as both techniques have advantages and disadvantages.

Keywords:

Lipectomy - Lipoma - Neck - Plastic surgery procedures - Lipomatosis, multiple symmetrical

Institution: Hospital das Clínicas da Universidade Federal de Pernambuco, Recife, PE, Brazil.




Publikationsverlauf

Eingereicht: 08. September 2023

Angenommen: 30. April 2024

Artikel online veröffentlicht:
20. Mai 2025

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)

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Bibliographical Record
PEDRO HENRIQUE DE ARAÚJO SILVA, JAIRO ZACCHÊ DE SÁ, FLÁVIO JOSÉ TEIXEIRA ROCHA ATAÍDE DA MOTTA, HELENA GABRIELE ALVES CASTRO, VINICYUS EDUARDO MELO AMORIM, ANDRESA DOS SANTOS VIANA, LARISSA CARARETO BRAVIN, PEDRO HENRIQUE PONTUAL. Lipectomia e lipoaspiração seriadas para manejo de síndrome de Madelung: A respeito de um caso. Revista Brasileira de Cirurgia Plástica (RBCP) – Brazilian Journal of Plastic Surgery 2024; 39: 217712352024rbcp0870pt.
DOI: 10.5935/2177-1235.2024RBCP0870-PT
 

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