Seltene Demenzerkrankungen: Frontotemporale Demenz

Abstract

Frontotemporal dementias (FTD) are among the rare dementias. Their symptomatology is - compared to the common Alzheimer’s disease - atypical, so that in many cases it takes a long time until a correct diagnosis is made. The following article gives an overview of the clinical symptoms, genetic and neuropathological basis, diagnostics and differential diagnostics and therapy.

Schlüsselwörter

frontotemporale Demenz - nicht-flüssige Aphasie - progrediente - semantische Demenz - primär progrediente Aphasien

Key words

frontotemporal dementia - non-fluent aphasia - progressive semantic dementia - primary progressive aphasia

Publication History

Article published online:
19 June 2023

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