Mitral annular disjunction

Mitral annular disjunction (MAD) refers to a structural abnormality of the mitral annulus in which a section of the mitral valve leaflets attaches to the atrial wall at a location away from the junction of the left atrial and left ventricular myocardium. Although first described in 1981 [Bharati S et al. Am Heart J 1981; 101 (5): 667], MAD has recently attracted more attention because of the growing body of evidence suggesting a potential relationship between MAD and ventricular arrhythmias and sudden cardiac death (SCD). It is most commonly diagnosed by transthoracic echocardiography, but findings may be subtle, and further cardiac imaging such as MRI may be necessary. Although not a very recent entity, it is possible that MAD may not be a well-known diagnostic consideration among the radiology community. To increase awareness for this abnormality, we present a previously asymptomatic young patient who needed cardiopulmonary resuscitation due to ventricular fibrillation. After a comprehensive evaluation, mitral valve prolapse (MVP) and MAD were found as the only culprits that may explain her malignant arrhythmia.

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Eingereicht: 09. Juli 2023

Angenommen nach Revision: 15. Oktober 2023

Artikel online veröffentlicht:
21. November 2023