Slow Progression of a Small Wilms’ Tumor

Abstract

We report the uncommon clinical course of a female with right-sided hemi-hyperplasia. At the age of 2 years and 2 months, a small spherical lesion of the right kidney was detected by ultrasound and magnetic resonance tomography. When the patient was 4 years and 7 months, the very slowly growing tumor was removed completely and diagnosed as intermediate risk stage I nephroblastoma. The case demonstrates that even small renal lesions require diagnostic work-up and adequate treatment.

Zusammenfassung

Wir berichten den ungewöhnlichen Verlauf einer Patientin mit rechtsseitiger Hemihypertrophie. Im Alter von 2 Jahren und 2 Monaten wurde erstmals eine sphärische Läsion der rechten Niere in Ultraschall und Kernspintomografie nachgewiesen. Im Alter von 4 Jahren und 7 Monaten erfolgte die vollständige nierenerhaltende Resektion der gering progredienten Raumforderung. Histologisch wurde ein Nephroblastom von intermediärer Histologie nachgewiesen. Der Fall zeigt, dass auch kleine renale Läsionen eine komplette Diagnostik und adäquate Behandlung erfordern.

Key words

Wilms' tumor - nephroblastoma - nephrogenic rest - hemi-hyperplasia

Schlüsselwörter

Wilms-Tumor - Nephroblastom - nephrogener Rest - Hemihypertrophie

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