Cor Triatriatum with Tetralogy of Fallot and Anomalous Drainage of Left Superior Vena Cava: A Case Report and Literature Review

Abstract

Cor triatriatum is a rare malformation, especially in association with tetralogy of Fallot, and has only been reported a few times in the literature. Due to the complexity of this abnormality, careful intraoperative exploration and a good differential diagnosis are crucial to select the appropriate surgical procedure. Here, we report a case with this rare combination of anomalies, an abnormal membranous septum above the mitral valve, and anomalous drainage of the left superior vena cava. The patient was successfully treated and achieved excellent hemodynamic parameters.

Keywords

cor triatriatum - tetralogy of Fallot - cardiac anatomy - congenital heart disease - CHD

• References

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