Zusammenfassung
Die aggressive intraabdominale Fibromatose ist eine seltene Reaktion auf chirurgische Traumata. Charakteristisch ist ein lokal destruierendes Wachstum ohne Metastasierung. Nur eine Operation im Sinne einer R0-Resektion führt zur Heilung. Es wird über einen 29-jährigen Patienten berichtet, bei dem es 19 Jahre nach Appendektomie und nach mehrfachen Relaparotomien aufgrund von Adhäsionen zur Ausbildung der aggressiven Fibromatose kam. Ein großer Konglomerattumor unter Einbeziehung des Ileum und des Kolon ascendens führte zu Darmobstruktion und Ileus. Eine komplette chirurgische Tumorentfernung führte nach primär komplizierten Verlauf zur Heilung.
Abstract
Aggressive intraabdominal fibromatosis is a rare response to surgical trauma. Characteristic is the local destroying growth. Only an operation in the purpose of R0-resection ends in cure. We report on a 29-year-old man, who developed intraabdominal fibromatosis as reaction to surgical trauma 19 years after appendectomy and subsquent to several relaparotomies due to adhesions. A huge conglomeratumor which included the ileum and the colon acsendens resulted in bowel obstruction and ileus. Complete surgical removal of the tumor lead after a primary complicated course to recovery.
Schlüsselwörter
Aggressive intraabdominelle Fibromatose - Ileus - Konglomerattumor - chirurgische Traumata
Key words
Aggressive intraabdominal fibromatosis - ileus - conglomerat tumor - surgical trauma
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Dr. med. Sabine Kersting
Klinik und Poliklinik für Allgemeine Chirurgie · Universitätsklinikum Münster
Waldeyerstr. 1
48149 Münster
Phone: 02 51/8 35 63 01
Fax: 02 51/8 35 64 14
Email: skerstin@uni-muenster.de
