DOI: 10.1055/s-00000075

Seminars in Respiratory and Critical Care Medicine

Issue 03 · Volume 37 · June 2016 DOI: 10.1055/s-006-31756 Orphan Lung Diseases Guest Editors: Jay H. Ryu, MD, and Luca Richeldi, MD

Preface

319
Ryu, Jay H.; Richeldi, Luca: Orphan Lung Diseases

321
Chu, Sarah G.; El-Chemaly, Souheil; Rosas, Ivan O.: Genetics and Idiopathic Interstitial Pneumonias
331
Lynch, Joseph P.; Huynh, Richard H.; Fishbein, Michael C.; Saggar, Rajan; Belperio, John A.; Weigt, S. Sam: Idiopathic Pulmonary Fibrosis: Epidemiology, Clinical Features, Prognosis, and Management
358
Puglisi, S.; Torrisi, S. E.; Giuliano, R.; Vindigni, V.; Vancheri, C.: What We Know About the Pathogenesis of Idiopathic Pulmonary Fibrosis
368
Antoniou, Katerina M.; Wuyts, Wim; Wijsenbeek, Marlies; Wells, Athol U.: Medical Therapy in Idiopathic Pulmonary Fibrosis
378
Tomassetti, Sara; Ryu, Jay H.; Piciucchi, Sara; Chilosi, Marco; Poletti, Venerino: Nonspecific Interstitial Pneumonia: What Is the Optimal Approach to Management?
395
Morell, Ferran; Villar, Ana; Ojanguren, Iñigo; Muñoz, Xavier; Cruz, María-Jesús: Hypersensitivity Pneumonitis: Challenges in Diagnosis and Management, Avoiding Surgical Lung Biopsy
406
Arcadu, Antonella; Moua, Teng; Yi, Eunhee S.; Ryu, Jay H.: Lymphoid Interstitial Pneumonia and Other Benign Lymphoid Disorders
421
Cordier, Jean-François; Cottin, Vincent; Lazor, Romain; Thivolet-Béjui, Françoise: Many Faces of Bronchiolitis and Organizing Pneumonia
457
Xu, Kai-Feng; Feng, Ruie; Cui, Han; Tian, Xinlun; Wang, Hanping; Zhao, Jing; Huang, Hui; Zhang, Weihong; Lo, Bee Hong: Diffuse Cystic Lung Diseases: Diagnostic Considerations