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Klin Monbl Augenheilkd 2024; 241(09): 1032-1038
DOI: 10.1055/a-2130-5131
Übersicht

Acute Idiopathic Blind Spot Enlargement Syndrome (AIBSES) in the Era of OCT – a Review

Article in several languages: deutsch | English
Julian Alexander Zimmermann 
Klinik für Augenheilkunde, Universitätsklinikum Münster, Deutschland
,
Julia Biermann 
Klinik für Augenheilkunde, Universitätsklinikum Münster, Deutschland
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Abstract

There are only about 100 case reports on the Acute Idiopathic Blind Spot Enlargement Syndrome (AIBSES). This is characterised by the eponymous visual field loss in the blind spot area, acute onset photopsia, and funduscopically little or no change in the optic disc area, with conspicuous outer retinal bands on optical coherence tomography (OCT). Typical is the unilateral occurrence. Predominantly young women are affected. While previous reviews of AIBSES either predate the introduction of OCT or focus on differentiation from potentially related outer retinal conditions (e.g., multiple evanescent white dot syndrome and acute zonal occult outer retinopathy), the present review will concentrate on the current perspective and treatment strategies that have been developed and will aim to help increase awareness. Since the first description of AIBSES in the late 1980s, the introduction of OCT has simplified the diagnosis and characterisation of AIBSES as a disease of the outer retina. Nevertheless, misdiagnosis remains common in the spectrum of optic neuritis, as AIBSES may be ignored in differential diagnosis.

Key words

retina - neuroophthalmology - intraocular inflammation


Publication History

Received: 18 December 2022

Accepted: 05 July 2023

Article published online:
07 September 2023

© 2023. Thieme. All rights reserved.

Georg Thieme Verlag KG
Rüdigerstraße 14, 70469 Stuttgart, Germany

 

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