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J Wrist Surg 2015; 04(04): 269-273
DOI: 10.1055/s-0035-1556861
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Bilateral Second Carpal Row Duplication Associated with Multiple Epiphyseal Dysplasia

Victoire Cladiere-Nassif
1   Hôpital Saint-Antoine, Paris, France
,
Caroline Delaroche
1   Hôpital Saint-Antoine, Paris, France
,
Edwige Pottier
2   Service de Radiologie, Hopital Saint-Antoine, Paris, France
,
Jean-Marc Feron
1   Hôpital Saint-Antoine, Paris, France
› Author Affiliations
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Publication History

Publication Date:
29 October 2015 (online)

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Abstract

We report a case of a 75-year-old woman presenting a hitherto undescribed condition of bilateral second carpal row duplication. She was diagnosed in childhood with both Marfan and Ehlers-Danlos syndromes, with no clear evidence and no further medical follow-up. She presented throughout her life with various articular symptoms, which appeared to be compatible with a diagnosis of multiple epiphyseal dysplasia, and underwent several surgical procedures on her knees and hips. Most recently, she was reporting pain at the base of the fifth metacarpal bone of the left hand. X-ray images and computed tomography (CT) were obtained for exploration and showed a total second row duplication in both carpi, with a total number of 18 carpal bones in each wrist.

Keywords

carpal duplication - epiphyseal dysplasia - capral malformation
 

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