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CC BY-NC-ND 4.0 · Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2019; 38(03): 199-202
DOI: 10.1055/s-0039-1693683
Case Report | Relato de Caso
Thieme Revinter Publicações Ltda Rio de Janeiro, Brazil

Orbital Schwannoma: Case Report and Review

Schwannoma de Órbita: Relato de caso e revisão
Ricardo Lourenço Caramanti
1   Centro do Cerebro e Coluna, São José do Rio Preto, SP, Brazil
,
Mário José Goes
2   Neurosurgery Department, Faculdade de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Feres Chaddad
3   Vascular Neurosurgery Department, Universidade de São Paulo, São Paulo, SP, Brazil
,
Lucas Crociati Meguins
2   Neurosurgery Department, Faculdade de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Dionei Freitas de Moraes
2   Neurosurgery Department, Faculdade de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Raysa Moreira Aprígio
2   Neurosurgery Department, Faculdade de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Sérgio Ivo Calzolari
2   Neurosurgery Department, Faculdade de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Carlos Eduardo Rocha
2   Neurosurgery Department, Faculdade de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Sebastião Carlos da Silva Jr.
2   Neurosurgery Department, Faculdade de São José do Rio Preto, São José do Rio Preto, SP, Brazil
› Author Affiliations
Further Information

Publication History

08 January 2019

27 May 2019

Publication Date:
25 July 2019 (online)

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Abstract

Orbital schwannomas are rare, presenting a rate of incidence between 1 and 5% of all orbital lesions. Their most common clinical symptoms are promoted by mass effect, such as orbital pain and proptosis. The best complementary exam is the magnetic resonance imaging (MRI), which shows low signal in T1, high signal in T2, and heterogeneous contrast enhancement. The treatment of choice is surgical, with adjuvant radiotherapy if complete resection is not possible. We report the case of a 24-year-old male patient with orbital pain and proptosis, without previous history of disease. The MRI showed a superior orbital lesion compatible with schwannoma, which was confirmed by biopsy after complete resection using a fronto-orbital approach.

Resumo

Schwannomas de órbita são raros, apresentando incidência entre 1 e 5% de todas as lesões de órbita. Seus sinais clínicos mais comuns são causados pelo efeito de massa da lesão, estando entre eles a dor orbitária e proptose. O melhor exame complementar é a ressonância magnética (MRI) que mostra uma lesão hipointensa em T1, hiperintensa em T2 e de captação heterogênea de contraste. O tratamento de escolha é cirúrgico, com uso de radioterapia adjuvante quando a ressecção completa não for possível. Neste estudo, relatamos, um paciente masculino de 24 anos com dor orbitária e proptose, sem historia de doenças prévias. A ressonância mostrou uma lesão na região superior da órbita comparável com um schwannoma, que foi confirmada por biópsia após a completa ressecção usando um acesso fronto orbitário.

Keywords

orbit - schwannoma - extraconal tumor

Palavras-chave

órbita - schwannoma - tumor extraconal
 

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