Intraokulare Raumforderungen im Kindesalter ohne Retinoblastom

Zusammenfassung

Die Diagnose kindlicher Augentumoren kann mitunter eine große Herausforderung darstellen, da insbesondere eine invasive Diagnostik über eine Biopsie zumindest bei der bestehenden Differenzialdiagnose eines Retinoblastoms kontraindiziert ist. Bei einem funktionslosen Auge mit unklarer, unilateraler Raumforderung gibt oftmals nur die Enukleation mit anschließender histopathologischer Aufarbeitung Aufschluss über die eigentliche Diagnose mit all den daraus resultierenden Konsequenzen. Der häufigste intraokulare Tumor im Kindesalter ist das Retinoblastom, wozu eine Reihe von Arbeiten zur nicht invasiven Diagnose veröffentlicht sind. Diese Arbeit beschäftigt sich deshalb mit den sehr viel selteneren anderen intraokularen Raumforderungen im Kindesalter, wobei insbesondere klinische Befunde, bildmorphologische Darstellungen und histopathologische Analysen der wichtigsten Tumorerkrankungen dargestellt werden.

Abstract

The diagnosis of an intraocular mass in children can be challenging as invasive procedures are not allowed, in particular if a retinoblastoma may be present. In eyes with a unilateral tumour mass and loss of function enucleation with subsequent histopathological processing might be the only option to establish a diagnosis and to exclude a malignant tumour. The present paper deals with intraocular tumours other than retinoblastoma in children, with a special focus on the correlation of modern imaging techniques and histopathological findings.

Schlüsselwörter

kindliche Augentumoren - bildgebende Diagnostik - Medulloepitheliome - Astrozytome - Morbus Coats

Key words

intraocular childhood malignancies - imaging process - medulloepithelioma - astrocytoma - Coatʼs disease

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