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Am J Perinatol 1999; Volume 16(Number 10): 0531-0536
DOI: 10.1055/s-1999-7279
Copyright © 1999 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA. Tel.: +1(212) 760-0888 x 132

APLASIA CUTIS CONGENITA IN AN INFANT OF AN INITIAL TRIPLET GESTATION: A CASE REPORT

Shonola S. Da-Silva1 , Eniola O. Fagbongbe2
  • Department of Pediatrics, Overlook Hospital-Atlantic Health Systems, Summit, New Jersey.
  • 1Current affiliation: Critical Care Fellow in Pediatrics at Montefiore Medical Center, Bronx, New York.
  • 2Current affiliation: Resident in Obstetrics & Gynecology at Jersey City Medical Center, Baldwin Avenue, Jersey City, New Jersey.
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Publication Date:
31 December 1999 (online)

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ABSTRACT

Aplasia cutis congenita (ACC) is the clinical manifestation of an uncommon group of skin disorders. One postulated etiology is disseminated intravascular coagulation from release of thrombogenic material arising from placental injury or fetal demise. This leads to disruption of the ectodermal blood supply responsible for the skin defects. We present a neonate with group V ACC, one of an initial triplet gestation, associated with fetal demise at 14 weeks and formation of a fetus papyraceus. The practice of selective fetal reduction as a result of multiple gestation seen with the use of fertility drugs may in theory increase the incidence of group V ACC.

KEYWORD

Aplasia cutis congenita - skin disorders - triplet gestation - fetus papyraceus