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Am J Perinatol 2003; 20(3): 121-124
DOI: 10.1055/s-2003-40011
Copyright © 2003 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA. Tel.: +1(212) 584-4662

Congenital Partial Pericardial Defect in a Neonate: A Case Report

Surasak Puvabanditsin1 , Eugene Garrow2 , Anjali Biswas1 , Angela Davydov1 , Manuel Gomez1 , Passara Liangthanasarn1
  • 1Department of Pediatrics, Jersey City Medical Center, New Jersey
  • 2Department of Surgery, Jersey City Medical Center, New Jersey
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Publication History

Publication Date:
12 June 2003 (online)

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ABSTRACT

This report describes a neonate with congenital partial absence of the pericardium associated with hypoplastic left heart syndrome. The patient presented with severe heart failure caused by a hypoplastic left ventricle. The infant died at 15 hours of age because of intractable congestive heart failure. Necropsy revealed, in addition to a hypoplastic left ventricle, a transverse biventricular constriction suggestive of partial absence of the pericardium. In addition to cardiovascular malformations, a left hydronephrosis and a bicornuate uterus was found. We report a rare clinical entity and review the literature.

KEYWORDS

Congenital partial pericardial defect - hypoplastic left heart syndrome - neonate

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