ABSTRACT
Congenital mesoblastic nephroma is a rare tumor of infancy that usually presents as
an asymptomatic abdominal mass. A full-term newborn infant with an atypical variant
of this neoplasm developed hemorrhagic shock and disseminated intravascular coagulation.
The stormy course was complicated by persistent fetal circulation and then the inability
to withdraw ventilatory support due to the mass effect of the tumor. After the removal
of the tumor at 10 days of age, transient conjugated hyperbilirubinemia developed.
At 15 months of age, the infant was thriving without evidence of recurrence of the
tumor.
