Optikusscheidenmeningeom mit 17 Jahren Amaurose

Summary

Amaurosis of the right eye occured in an 18-year-old women. 17 years later the healthy patient was referred for diagnosis, showing an amaurotic pupil, no protrusion, normal motility and corneal sensitivity, normal morphology of the anterior segment. In ophthalmoscopy optic atrophy with typical retinociliary collateral vessels, calcified and obliterated vessels throughout to the posterior pole and a macular scar. In fluoresceine angiography normal choroidal filling, greatly diminuished retinal capillary filling, hypofluorescent optical disc with venous shunt to retinociliary collaterals, no preretinal neovascularizations. On cranial CT and nuclear magnetic imaging pathognomonic meningeoma of the optic nerve sheaths with tram-tracking lines. Inspite of suprasellar extension no indication to surgical therapy because of normal hormone production.

Schlüsselwörter

Optikusscheidenmeningeom - einfache Optikusatrophie mit Kollateralbildung - optikoziliare Venen - Frisen-Zeichen - Gliome

Key words

Optic nerve sheath meningeoma - optic nerve atrophy - opticociliary vessels - Frisen sign - glioma