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J Am Acad Audiol 2000; 11(09): 484-488
DOI: 10.1055/s-0042-1748140
Original Article

A Case of Susac Syndrome

M. Wende Yellin
Department of Speech Pathology and Audiology, Northern Arizona University, Flagstaff, Arizona
,
Thomas W. Johnson
Coconino Neurology Services, Flagstaff, Arizona
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Abstract

Susac syndrome is a readily recognized but often misdiagnosed disorder almost exclusively affecting women in the 20- to 40–year age range. Characterized by the clinical triad of encephalopathy, branch retinal artery occlusions, and sensorineural hearing loss, patients with Susac syndrome are often misdiagnosed with multiple sclerosis (MS). Unlike MS, however, the disease process extends over a 1- to 2–year period and then goes into remission. This presentation describes the progression of symptoms of a patient eventually diagnosed with Susac syndrome.

Abbreviations: ALD = assistive listening device, EEG = electroencephalogram, MRI = magnetic resonance imaging, MS = multiple sclerosis

Key Words

Branch retinal artery occlusion - encephalopathy - sensorineural hearing loss - Susac syndrome


Publication History

Article published online:
14 April 2022

© 2000. American Academy of Audiology. This article is published by Thieme.

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