Infantile Fibrosarcoma: Surgical Treatment and MRI/MRA Findings

Introduction

Congenital, infantile, or juvenile fibrosarcoma is a rare, soft tissue tumor which can occur between birth and 15 years of age [1]. Some authors only consider those cases diagnosed before the age of 2 as infantile fibrosarcoma [2]. Congenital fibrosarcoma tends not to metastasize (<10 percent) and long-term survival is good. Infantile fibrosarcoma (IFS) lesions are typically large tumors that grow rapidly [3]. Clinically these tumors are highly vascularized and may have superficial ulcerations and bleeding, which makes it difficult to differentiate them from hemangiomas. Treatment is primarily surgical and consists of wide local resection. This case report illustrates the surgical treatment of an infant with an upper extremity fibrosarcoma and the difficulty in differentiating this tumor from other vascular tumors. The role of MR imaging including MR angiography for diagnosis and follow-up is discussed.

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