Eur J Pediatr Surg 2010; 20(6): 423-425
DOI: 10.1055/s-0030-1254144
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Endobronchial, Pulmonary and Liver Leiomyomata in a Child with Primary Immune Deficiency

I. R. User1 , D. Dogru2 , B. Talim3 , D. Orhan3 , I. Karnak1
  • 1Hacettepe University, Department of Pediatric Surgery, Ankara, Turkey
  • 2Hacettepe University, Department of Pediatric Pulmonology, Ankara, Turkey
  • 3Hacettepe University, Department of Pediatric Pathology, Ankara, Turkey
Further Information

Publication History

Publication Date:
07 June 2010 (online)

Introduction

Leiomyoma of the lung is a rare benign tumor in children [8]. It is associated with immune suppression after organ transplantation and viral infections such as Eppstein-Barr virus (EBV) and HIV [4]. It is of mesodermal origin and it has been hypothesized that leiomyoma of the lung arises from the smooth muscles of the bronchial wall or artery [2]. Half of these tumors are parenchymal and the rest of the lesions are endobronchial or tracheal [5]. Symptoms include bronchial obstruction and atelectasis, and the lesions can be the cause of recurrent pulmonary infections, but they are otherwise coincidentally found [3] [7]. We present the first case of a child with a primary immune deficiency and EBV-negative serology and endobronchial, pulmonary and liver leiomyomata to emphasize the importance of planning before surgery and the necessity of investigating for associated leiomyomata.

References

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Correspondence

Dr. Ibrahim Karnak

Hacettepe University

Department of Pediatric Surgery

06100 Ankara

Turkey

Phone: + 90 312 311 5541

Fax: + 90 312 311 5541

Email: ikarnak@hacettepe.edu.tr