Eur J Pediatr Surg 2014; 24(04): 350-352
DOI: 10.1055/s-0032-1324695
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Georg Thieme Verlag KG Stuttgart · New York

Fatal Complication after Repair of a Congenital Diaphragmatic Hernia Associated with Hepatopulmonary Fusion, Anomalous Right Pulmonary Venous Return, and Azygos Continuation of the Inferior Vena Cava

Joshua Hamilton
1  Department of Surgery, Phoenix Integrated Surgical Residency, Phoenix, Arizona, United States
,
Dawn Jaroszewski
2  Department of Surgery, Mayo Clinic, Scottsdale, Arizona, United States
,
David Notrica
2  Department of Surgery, Mayo Clinic, Scottsdale, Arizona, United States
3  Department of Surgery, Phoenix Children's Hospital, Phoenix, Arizona, United States
4  Department of Surgery, University of Arizona College of Medicine, Phoenix, Arizona, United States
› Author Affiliations
Further Information

Publication History

25 November 2011

27 June 2012

Publication Date:
23 October 2012 (eFirst)

Conclusions

Primary HPF is an extremely rare condition in patients with a right-sided CDH. When this finding is suspected or encountered at surgery, complete radiological imaging should be performed before surgical correction to identify possible aberrant venous and arterial anatomy. Retaining a portion of the fusion and only partial closure of the defect may be reasonable to prevent catastrophic complications.