Fatal Complication after Repair of a Congenital Diaphragmatic Hernia Associated with Hepatopulmonary Fusion, Anomalous Right Pulmonary Venous Return, and Azygos Continuation of the Inferior Vena Cava

Conclusions

Primary HPF is an extremely rare condition in patients with a right-sided CDH. When this finding is suspected or encountered at surgery, complete radiological imaging should be performed before surgical correction to identify possible aberrant venous and arterial anatomy. Retaining a portion of the fusion and only partial closure of the defect may be reasonable to prevent catastrophic complications.

• References

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