Zusammenfassung
Glaukomerkrankungen im Kindesalter sind selten. Da ohne Behandlung in der Regel die
Erblindung eintritt, ist eine umgehende Diagnosestellung und Therapie von höchster
Bedeutung. Die
Heterogenität der Erkrankung erfordert eine genaue Kenntnis der möglichen Ursachen
und deren individuelle Behandlung. Dieser Artikel soll einen Überblick über die kindlichen
Glaukome
vermitteln und die wichtigsten Aspekte der Therapie aufzeigen.
Abstract
Childhood glaucoma is a rare disease. Since a lacking therapy normally leads to blindness
an immediate diagnosis and appropriate treatment are crucial. The heterogeneity of
childhood
glaucoma requires a comprehensive knowledge of possible underlying pathomechanisms
of primary and secondary childhood glaucoma types. Several types of childhood glaucoma
are accompanied with
ocular or systemic syndromes and hereditary causes are frequent. Thus, an interdisciplinary
team of ophthalmologists, orthoptists, pediatricians, human geneticists, and anesthesiologists
is
vital for a successful supply. Most cases rely on a dysgenesis of trabecular
meshwork with impaired outflow. Thus, usually a surgical approach is indicated. To
handle a surgery in a
buphthalmic eye an experienced hand is required. Special attention should be
paid on the correct prescription of topical antiglaucomatous therapy in children since
they are more prone to
develop side effects. This article aims to provide an overview about the different
childhood glaucoma types and to point out the most important aspects of their individual
treatment
strategies.
Schlüsselwörter
Primäres kongenitales Glaukom - Vorderabschnittsdysgenesie - CYP1B1 - Narkoseuntersuchung
- Trabekulotomie
Key words
Primary congenital glaucoma - anterior segment dysgenesis - CYP1B1 - examination under
anesthesia - trabeculotomy
