A boy aged 2 years and 7 months who had undergone duodeno-duodenostomy for duodenal
atresia and annular pancreas in the neonatal period presented with recurrent pancreatitis.
ERCP showed an incomplete pancreas divisum associated with pancreaticobiliary maljunction.
At 3 years and 8 months of age, we performed a Frey procedure in combination with
total excision of the extrahepatic bile duct. The main pancreatic duct was opened
in the body and the head was cored out anteriorly. The pancreaticobiliary system was
reconstructed with a Roux-en-Y anastomosis. The patient has been free from symptoms
with excellent weight gain in the follow-up period of 20 months. The Frey procedure
can be a safe and effective operation in children with chronic pancreatitis caused
by complex pancreatobiliary disorders associated with duodenal atresia.
chronic pancreatitis - pancreas divisum - pancreaticobiliary maljunction - Frey procedure
- children