Congenital Absence of the Portal Vein: A Complex Disease with Multiple Manifestations and Types of Treatment

Introduction

Congenital absence of the portal vein is a rare condition in which the mesenteric and splenic venous circulation bypasses the liver and drains directly into the systemic circulation [1] [2] [3] [4] [5]. We report on this malformation in 2 patients, a child and an adult, with unusual clinical presentations and positive outcomes.

References

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