Eur J Pediatr Surg 1989; 44(3): 166-168
DOI: 10.1055/s-2008-1043227
Case report

© Georg Thieme Verlag KG Stuttgart · New York

Adrenocortical Carcinoma in a Child with Congenital Hemihypertrophy

Adrenokortikales Karzinom bei einem Kind mit kongenitaler HemihypertrophieS.  Ogita1 , K.  Tokiwa1 , T.  Takahashi1 , A.  Kinugasa2 , T.  Sawada2
  • 1Division of Surgery, Children's Research Hospital, Kyoto Prefectural University of Medicine
  • 2Department of Pediatrics, Kyoto Prefectural University of Medicine, Kyoto, Japan
Further Information

Publication History

Publication Date:
25 March 2008 (online)

Abstract

We describe a very rare case of adrenocortical carcinoma (ACC) presenting with Cushing's virilising syndrome in a female child with congenital hemihypertrophy (CHh). CHh was of more value for early detection of ACC than Cushing's virilisation.

Zusammenfassung

Es wird der seltene Fall eines adrenokortikalen Karzinomes mit Cushing-Syndrom vorgestellt. Bei dem Mädchen bestand eine angeborene Hemihypertrophie.

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